Klippel-Trénaunay syndrome, pregnancy and the liver: an unusual interplay

Abstract

Klippel-Trénaunay syndrome is a rare congenital syndrome characterized by capillary malformations, soft tissue and bone hypertrophy, and varicose veins. There is a well-established risk for thrombotic complications in these patients. A case of a young patient diagnosed post partum with the very rare liver involvement is presented. The complex clinical course, the multidisciplinary management and the long-term outcome are discussed.

Keywords Klippel-Trénaunay syndrome, portal vein thrombosis, varicose veins, pregnancy